Fontan-associated liver disease: screening, management, and transplant considerations

J Emamaullee, AN Zaidi, T Schiano, J Kahn… - Circulation, 2020 - Am Heart Assoc
Surgical innovation and multidisciplinary management have allowed children born with
univentricular physiology congenital heart disease to survive into adulthood. An estimated …

MR elastography of liver: current status and future perspectives

IS Idilman, J Li, M Yin, SK Venkatesh - Abdominal Radiology, 2020 - Springer
Non-invasive evaluation of liver fibrosis has evolved over the last couple of decades.
Currently, elastography techniques are the most widely used non-invasive methods for …

Fontan‐associated liver disease

MB Hilscher, ML Wells, SK Venkatesh, F Cetta… - …, 2022 - Wiley Online Library
Fontan-associated liver disease (FALD) is a form of congestive hepatopathy that is universal
among patients who have undergone Fontan palliation for functional single ventricle …

Magnetic resonance elastography of the liver: everything you need to know to get started

KM Pepin, CL Welle, FF Guglielmo, JR Dillman… - Abdominal …, 2022 - Springer
Magnetic resonance elastography (MRE) of the liver has emerged as the non-invasive
standard for the evaluation of liver fibrosis in chronic liver diseases (CLDs). The utility of …

EASL-ERN position paper on liver involvement in patients with Fontan-type circulation

L Téllez, A Payancé, E Tjwa, MJ Del Cerro, L Idorn… - Journal of …, 2023 - Elsevier
Fontan-type surgery is the final step in the sequential palliative surgical treatment of infants
born with a univentricular heart. The resulting long-term haemodynamic changes promote …

Issues in multi-organ transplantation of the liver with kidney or heart in polycystic liver-kidney disease or congenital heart disease: Current practices and …

T Taner, MB Hilscher, CR Broda, JPH Drenth - Journal of hepatology, 2023 - Elsevier
Solid organ transplantation has become an integral part of the management of patients with
end-stage diseases of the kidney, liver, heart and lungs. Most procedures occur in isolation …

Imaging of Fontan-associated liver disease

JR Dillman, AT Trout, T Alsaied, A Gupta, AM Lubert - Pediatric radiology, 2020 - Springer
The Fontan operation has dramatically altered the natural history of functionally single
ventricle congenital heart disease. Patients who have undergone the Fontan operation are …

Elastography for pediatric chronic liver disease: a review and expert opinion

G Ferraioli, RG Barr, JR Dillman - Journal of Ultrasound in …, 2021 - Wiley Online Library
In adults with chronic liver diseases, ultrasound and magnetic resonance shear wave
elastography (SWE) can replace liver biopsy in several clinical scenarios. Several …

Myocardial fibrosis, diastolic dysfunction and elevated liver stiffness in the Fontan circulation

T Alsaied, RA Moore, SM Lang, V Truong… - Open …, 2020 - openheart.bmj.com
Introduction Single ventricle diastolic dysfunction and hepatic fibrosis are frequently
observed in patients with a Fontan circulation. The relationship between adverse …

Haemodynamic and prognostic associations of liver fibrosis scores in Fontan-associated liver disease

IM De Miguel, PS Kamath, AC Egbe, CC Jain, F Cetta… - Heart, 2023 - heart.bmj.com
Objectives Fontan-associated liver disease (FALD) is universal post-Fontan palliation;
however, its impact on survival remains controversial and current diagnostic tools have …