Neurofibromatosis (NF) is a neurocutaneous syndrome characterized by the development of
tumors of the central or peripheral nervous system including the brain, spinal cord, organs …

Vestibular schwannoma (VS) is a Schwann cell-derived tumour arising from the
vestibulocochlear nerve. Although benign, it represents a threat to intracranial structures due …

Neurofibromatosis type 2 is an often devastating autosomal dominant disorder which, until
relatively recently, was confused with its more common namesake neurofibromatosis type 1 …

Abstract Neurofibromatosis type 2 (NF2) is a genetic condition marked by the development
of multiple benign tumors in the nervous system. The most common tumors associated with …

Schwannomas are slow-growing benign neoplasms that develop throughout the body
causing pain, sensory/motor dysfunction, and death. Because bacterial immunotherapy has …

Abstract Neurofibromatosis Type 2 (NF2) is a rare tumor disorder caused by pathogenic
variants of the merlin tumor suppressor encoded by NF2. Patients develop vestibular …

Abstract Neurofibromatosis type I (NF1), neurofibromatosis type 2 (NF2), and
schwannomatosis represent a diverse group of genetic tumor predisposition syndromes with …

Although diagnosis and treatment of vestibular schwannomas (VSs) improved in recent
years, no factors have yet been identified as being capable of predicting tumor growth …

Genetic syndromes which develop one or more nervous system (NS) tumors as one of the
manifestations can be grouped under the umbrella term of NS tumor predisposition …

Simple Summary The neurofibromatoses—neurofibromatosis type 1, neurofibromatosis type
2, and schwannomatosis—are genetic tumor predisposition syndromes in which affected …