Cystic kidneys are common causes of end-stage renal disease, both in children and in
adults. Autosomal dominant polycystic kidney disease (ADPKD) and autosomal recessive …

Autosomal-dominant polycystic kidney disease (ADPKD) affects up to 12 million individuals
and is the fourth most common cause for renal replacement therapy worldwide. There have …

Clinical vignette A 41-year old female underwent a computed tomography (CT) scan in 2010
because of symptoms suggestive of appendicitis. Incidentally, multiple liver lesions …

Polycystic liver disease (PLD) is the result of embryonic ductal plate malformation of the
intrahepatic biliary tree. The phenotype consists of numerous cysts spread throughout the …

The advent of enhanced radiological imaging techniques has facilitated the diagnosis of
cystic liver lesions. Concomitantly, the evidence base supporting the management of these …

Polycystic liver diseases (PLDs) are inherited genetic disorders characterized by
progressive development of intrahepatic, fluid-filled biliary cysts (more than ten), which …

Background & Aims Polycystic liver disease (PLD), the most common extrarenal
manifestation of autosomal-dominant polycystic kidney disease (ADPKD), has become more …

Polycystic liver diseases are genetic disorders characterized by progressive bile duct
dilatation and/or cyst development. The large volume of hepatic cysts causes different …

Cystic hepatic lesions are commonly encountered in daily practice. The diagnosis of these
lesions ranges from benign lesions of no clinical significance to malignant and potentially …

Background & Aims Polycystic liver disease is the most common extrarenal manifestation of
autosomal dominant polycystic kidney disease (ADPKD). There is need for robust long-term …