Management of phaeochromocytoma and paraganglioma in patients with germline SDHB pathogenic variants: an international expert Consensus statement

D Taïeb, S Nölting, ND Perrier, M Fassnacht… - Nature Reviews …, 2024 - nature.com
Adult and paediatric patients with pathogenic variants in the gene encoding succinate
dehydrogenase (SDH) subunit B (SDHB) often have locally aggressive, recurrent or …

Lutathera® Orphans: State of the Art and Future Application of Radioligand Therapy with 177Lu-DOTATATE

L Urso, A Nieri, L Uccelli, A Castello, P Artioli, C Cittanti… - Pharmaceutics, 2023 - mdpi.com
Lutathera® is the first EMA-and FDA-approved radiopharmaceutical for radioligand therapy
(RLT). Currently, on the legacy of the NETTER1 trial, only adult patients with progressive …

Differential diagnosis of cardiac tumors: general consideration and echocardiographic approach

PG Pino, A Moreo, C Lestuzzi - Journal of Clinical Ultrasound, 2022 - Wiley Online Library
Cardiac tumors may be primary (either benign or malignant) or secondary (malignant) and
are first detected by echocardiography in most cases. The cardiologist often challenges their …

Approach to the patient: concept and application of targeted radiotherapy in the paraganglioma patient

K Pacak, D Taieb, FI Lin, A Jha - The Journal of Clinical …, 2024 - academic.oup.com
Paragangliomas can metastasize, posing potential challenges both in symptomatic
management and disease control. Systemic targeted radiotherapies using 131I-MIBG and …

18F-MFBG PET/CT is an effective alternative of 68Ga-DOTATATE PET/CT in the evaluation of metastatic pheochromocytoma and paraganglioma

P Wang, T Li, Y Cui, H Zhuang, F Li… - Clinical Nuclear …, 2023 - journals.lww.com
Purpose The current guidelines state that the functional imaging choice in the evaluation of
metastatic pheochromocytoma and paraganglioma (PPGL) is 68 Ga-DOTATATE PET/CT. 18 …

Image-guided precision medicine in the diagnosis and treatment of pheochromocytomas and paragangliomas

G Gabiache, C Zadro, L Rozenblum, D Vezzosi… - Cancers, 2023 - mdpi.com
Simple Summary Pheochromocytomas and paragangliomas are rare neural-crest-derived
tumors with variable prognosis. In an era of tailored treatment strategies, medical imaging …

Systemic radiopharmaceutical therapy of pheochromocytoma and paraganglioma

JA Carrasquillo, CC Chen, A Jha, K Pacak… - Journal of Nuclear …, 2021 - Soc Nuclear Med
Whereas benign pheochromocytomas and paragangliomas are often successfully cured by
surgical resection, treatment of metastatic disease can be challenging in terms of both …

Pediatric metastatic pheochromocytoma and paraganglioma: Clinical presentation and diagnosis, genetics, and therapeutic approaches

MJM Kuo, MA Nazari, A Jha, K Pacak - Frontiers in Endocrinology, 2022 - frontiersin.org
Although pediatric pheochromocytomas and paragangliomas (PPGLs) are rare, they have
important differences compared to those in adults. Unfortunately, without timely diagnosis …

[PDF][PDF] Choice Is Good at Times: The Emergence of [64Cu] Cu-DOTATATE–Based Somatostatin Receptor Imaging in the Era of [68Ga] Ga-DOTATATE

A Jha, M Patel, JA Carrasquillo, CC Chen… - Journal of Nuclear …, 2022 - Soc Nuclear Med
Somatostatin receptor (SSTR) imaging has brought about impactful changes in clinical
management of neuroendocrine tumors (NETs), including pheochromocytoma and …

Management of pheochromocytomas and paragangliomas

JE Passman, H Wachtel - Surgical Clinics, 2024 - surgical.theclinics.com
Pheochromocytomas and paragangliomas (PPGLs) are catecholamine-producing
neuroendocrine tumors derived from chromaffin cells. 1–3 Pheochromocytomas are derived …