Calcium signaling and cardiac arrhythmias

AP Landstrom, D Dobrev, XHT Wehrens - Circulation research, 2017 - Am Heart Assoc
There has been a significant progress in our understanding of the molecular mechanisms by
which calcium (Ca2+) ions mediate various types of cardiac arrhythmias. A growing list of …

Hypertrophic cardiomyopathy: an overview of genetics and management

P Teekakirikul, W Zhu, HC Huang, E Fung - Biomolecules, 2019 - mdpi.com
Hypertrophic cardiomyopathy (HCM) is a genetically heterogeneous cardiac muscle
disorder with a diverse natural history, characterized by unexplained left ventricular …

Evolutionary conservation and expression of human RNA-binding proteins and their role in human genetic disease

S Gerstberger, M Hafner, M Ascano… - Systems biology of RNA …, 2014 - Springer
RNA-binding proteins (RBPs) are effectors and regulators of posttranscriptional gene
regulation (PTGR). RBPs regulate stability, maturation, and turnover of all RNAs, often …

Variant interpretation for dilated cardiomyopathy: refinement of the American College of Medical Genetics and Genomics/ClinGen Guidelines for the DCM Precision …

A Morales, DD Kinnamon, E Jordan, J Platt… - Circulation: Genomic …, 2020 - Am Heart Assoc
Background: The hypothesis of the Dilated Cardiomyopathy Precision Medicine Study is that
most dilated cardiomyopathy has a genetic basis. The study returns results to probands and …

Mutations in alpha-actinin-2 cause hypertrophic cardiomyopathy: a genome-wide analysis

C Chiu, RD Bagnall, J Ingles, L Yeates… - Journal of the American …, 2010 - jacc.org
Objectives: This study describes a genome-wide linkage analysis of a large family with
clinically heterogeneous hypertrophic cardiomyopathy (HCM). Background: Familial HCM is …

Heart plasticity in response to pressure-and volume-overload: a review of findings in compensated and decompensated phenotypes

FG Pitoulis, CM Terracciano - Frontiers in Physiology, 2020 - frontiersin.org
The adult human heart has an exceptional ability to alter its phenotype to adapt to changes
in environmental demand. This response involves metabolic, mechanical, electrical, and …

Mutation type is not clinically useful in predicting prognosis in hypertrophic cardiomyopathy

AP Landstrom, MJ Ackerman - Circulation, 2010 - Am Heart Assoc
The sentinel discovery of a genetic locus responsible for familial HCM was identified in 1989
by Jarcho and colleagues. 6 Jarcho used linkage analysis of a large, multigenerational …

[HTML][HTML] Clinical predictors of genetic testing outcomes in hypertrophic cardiomyopathy

J Ingles, T Sarina, L Yeates, L Hunt, I Macciocca… - Genetics in …, 2013 - Elsevier
Purpose Genetic testing for hypertrophic cardiomyopathy has been commercially available
for almost a decade; however, low mutation detection rate and cost have hindered uptake …

Molecular genetics and pathogenesis of cardiomyopathy

A Kimura - Journal of human genetics, 2016 - nature.com
Cardiomyopathy is defined as a disease of functional impairment in the cardiac muscle and
its etiology includes both extrinsic and intrinsic factors. Cardiomyopathy caused by the …

Multiple loci are associated with white blood cell phenotypes

MA Nalls, DJ Couper, T Tanaka, FJA van Rooij… - PLoS …, 2011 - journals.plos.org
White blood cell (WBC) count is a common clinical measure from complete blood count
assays, and it varies widely among healthy individuals. Total WBC count and its constituent …