Progressive pulmonary fibrosis: an expert group consensus statement

SK Rajan, V Cottin, R Dhar, S Danoff… - European …, 2023 - Eur Respiratory Soc
This expert group consensus statement emphasises the need for standardising the definition
of progressive fibrosing interstitial lung diseases (F-ILDs), with an accurate initial diagnosis …

[HTML][HTML] Idiopathic pulmonary fibrosis: best practice in monitoring and managing a relentless fibrotic disease

WA Wuyts, M Wijsenbeek, B Bondue, D Bouros… - Respiration, 2020 - karger.com
Idiopathic pulmonary fibrosis (IPF) is a fibrosing interstitial lung disease that is, by definition,
progressive. Progression of IPF is reflected by a decline in lung function, worsening of …

Real-world experience with nintedanib in patients with idiopathic pulmonary fibrosis

E Brunnemer, J Wälscher, S Tenenbaum… - Respiration, 2018 - karger.com
Background: Nintedanib, an oral tyrosine kinase inhibitor, has been shown to slow down the
progression of idiopathic pulmonary fibrosis (IPF) in two randomised placebo-controlled …

Oxygen in patients with fibrotic interstitial lung disease: an international Delphi survey

RK Lim, C Humphreys, J Morisset… - European …, 2019 - Eur Respiratory Soc
Rationale Patients with fibrotic interstitial lung disease (ILD) frequently develop resting or
exertional hypoxaemia. There is heterogeneity in clinical practice and a paucity of evidence …

The effect of anti-acid therapy on survival in idiopathic pulmonary fibrosis: a methodological review of observational studies

T Tran, S Suissa - European respiratory journal, 2018 - Eur Respiratory Soc
International treatment guidelines for idiopathic pulmonary fibrosis (IPF) give a conditional
recommendation for anti-acid therapy. As some observational studies reported discrepant …

Oxygen therapy in COPD and interstitial lung disease: navigating the knowns and unknowns

YH Khor, EA Renzoni, D Visca… - ERJ open …, 2019 - Eur Respiratory Soc
Domiciliary oxygen therapy is often prescribed for patients with hypoxaemia due to
advanced lung disease, most commonly chronic obstructive pulmonary disease (COPD) and …

Ongoing challenges in pulmonary fibrosis and insights from the nintedanib clinical programme

C Valenzuela, SE Torrisi, N Kahn, M Quaresma… - Respiratory …, 2020 - Springer
The approvals of nintedanib and pirfenidone changed the treatment paradigm in idiopathic
pulmonary fibrosis (IPF), and increased our understanding of the underlying disease …

Guidelines of the Polish Respiratory Society for diagnosis and treatment of idiopathic pulmonary fibrosis

WJ Piotrowski, I Bestry, AJ Białas… - Advances in …, 2020 - journals.viamedica.pl
Introduction: This document presents the guidelines of the Polish Respiratory Society
(PTChP, Polskie Towarzystwo Chorób Płuc) for diagnosis and treatment of idiopathic …

Longitudinal changes in clinical features, management, and outcomes of idiopathic pulmonary fibrosis. A nationwide cohort study

SW Moon, SY Kim, MP Chung, H Yoo… - Annals of the …, 2021 - atsjournals.org
Rationale: In recent decades, diagnosis and treatment recommendations for idiopathic
pulmonary fibrosis (IPF) have changed. In Korea, the average life expectancy has increased …

Guidelines of the polish respiratory society on the diagnosis and treatment of progressive fibrosing interstitial lung diseases other than idiopathic pulmonary fibrosis

WJ Piotrowski, MM Martusewicz-Boros… - … in Respiratory Medicine, 2022 - mdpi.com
Highlights The working group of the Polish Respiratory Society (PTChP) developed
guidelines for diagnosis and treatment of PF-ILD. What are the main findings? A …