[HTML][HTML] BRCA mutations in ovarian and prostate cancer: bench to bedside

S Boussios, E Rassy, M Moschetta, A Ghose… - Cancers, 2022 - mdpi.com
Simple Summary DNA damage is one of the hallmarks of cancer. Epithelial ovarian cancer
(EOC)—especially the high-grade serous subtype—harbors a defect in at least one DNA …

[HTML][HTML] Endogenous DNA damage as a source of genomic instability in cancer

A Tubbs, A Nussenzweig - Cell, 2017 - cell.com
Genome instability, defined as higher than normal rates of mutation, is a double-edged
sword. As a source of genetic diversity and natural selection, mutations are beneficial for …

Whole genome, transcriptome and methylome profiling enhances actionable target discovery in high-risk pediatric cancer

M Wong, C Mayoh, LMS Lau, DA Khuong-Quang… - Nature medicine, 2020 - nature.com
Abstract The Zero Childhood Cancer Program is a precision medicine program to benefit
children with poor-outcome, rare, relapsed or refractory cancer. Using tumor and germline …

[HTML][HTML] Genomic predictors of response to PD-1 inhibition in children with germline DNA replication repair deficiency

A Das, S Sudhaman, D Morgenstern, A Coblentz… - Nature medicine, 2022 - nature.com
Cancers arising from germline DNA mismatch repair deficiency or polymerase proofreading
deficiency (MMRD and PPD) in children harbour the highest mutational and microsatellite …

[HTML][HTML] Analysis of 100,000 human cancer genomes reveals the landscape of tumor mutational burden

ZR Chalmers, CF Connelly, D Fabrizio, L Gay, SM Ali… - Genome medicine, 2017 - Springer
Background High tumor mutational burden (TMB) is an emerging biomarker of sensitivity to
immune checkpoint inhibitors and has been shown to be more significantly associated with …

[HTML][HTML] Integrated molecular meta-analysis of 1,000 pediatric high-grade and diffuse intrinsic pontine glioma

A Mackay, A Burford, D Carvalho, E Izquierdo… - Cancer cell, 2017 - cell.com
We collated data from 157 unpublished cases of pediatric high-grade glioma and diffuse
intrinsic pontine glioma and 20 publicly available datasets in an integrated analysis of> …

[HTML][HTML] Comprehensive analysis of hypermutation in human cancer

BB Campbell, N Light, D Fabrizio, M Zatzman, F Fuligni… - Cell, 2017 - cell.com
We present an extensive assessment of mutation burden through sequencing analysis of>
81,000 tumors from pediatric and adult patients, including tumors with hypermutation caused …

DNA mismatch repair in cancer

M Baretti, DT Le - Pharmacology & therapeutics, 2018 - Elsevier
Microsatellite instability (MSI) refers to the hypermutator phenotype secondary to frequent
polymorphism in short repetitive DNA sequences and single nucleotide substitution, as …

Immune checkpoint inhibition for hypermutant glioblastoma multiforme resulting from germline biallelic mismatch repair deficiency

E Bouffet, V Larouche, BB Campbell… - Journal of clinical …, 2016 - ascopubs.org
Purpose Recurrent glioblastoma multiforme (GBM) is incurable with current therapies.
Biallelic mismatch repair deficiency (bMMRD) is a highly penetrant childhood cancer …

Infant high-grade gliomas comprise multiple subgroups characterized by novel targetable gene fusions and favorable outcomes

M Clarke, A Mackay, B Ismer, JC Pickles… - Cancer discovery, 2020 - AACR
Infant high-grade gliomas appear clinically distinct from their counterparts in older children,
indicating that histopathologic grading may not accurately reflect the biology of these tumors …