It is well established that portal hypertension can occur in the absence of cirrhosis, as
reported in patients with immune disorders, infections and thrombophilia. However, similar …

Idiopathic non-cirrhotic portal hypertension (INCPH) is a clinicopathologic disease entity
characterized by the presence of clinical signs and symptoms of portal hypertension (PH) in …

Portal hypertension in the absence of portal vein thrombosis and without cirrhosis, but with
mild or moderate alterations of liver histology (eg, obliterative venopathy, nodular …

Portal hypertension (PH), defined as a pathological increase in the portal vein pressure, has
different aetiologies and causes. Intrahepatic PH is mostly secondary to the presence of …

Portal hypertension is a major contributor to decompensation and death from liver disease, a
global health problem. Here, we demonstrate homozygous damaging mutations in GIMAP5 …

Acyl CoA Oxidase 2 (ACOX2) encodes branched-chain acyl-CoA oxidase, a peroxisomal
enzyme believed to be involved in the metabolism of branched-chain fatty acids and bile …

Idiopathic portal hypertension (IPH) is a rare disorder characterized by clinical portal
hypertension in the absence of a recognizable cause such as cirrhosis. Laboratory tests …

Abstract Background and Aims: Porto-sinusoidal vascular disorder (PSVD) is a group of liver
vascular diseases featuring lesions encompassing the portal venules and sinusoids …

The landscape of chronic liver disease has drastically changed over the past 20 years,
largely due to advances in antiviral therapy and the rise of metabolic syndrome and …

Background & Aims Porto-sinusoidal vascular disease (PSVD) is a rare vascular liver
disease of unknown etiology that causes portal hypertension. It usually affects young …