Pulmonary alveolar proteinosis
BC Trapnell, K Nakata, F Bonella, I Campo… - Nature Reviews …, 2019 - nature.com
Pulmonary alveolar proteinosis (PAP) is a syndrome characterized by the accumulation of
alveolar surfactant and dysfunction of alveolar macrophages. PAP results in progressive …
alveolar surfactant and dysfunction of alveolar macrophages. PAP results in progressive …
Pulmonary alveolar proteinosis–current and future therapeutical strategies
LB Jehn, F Bonella - Current Opinion in Pulmonary Medicine, 2023 - journals.lww.com
Pulmonary alveolar proteinosis – current and future therapeu... : Current Opinion in Pulmonary
Medicine Pulmonary alveolar proteinosis – current and future therapeutical strategies : Current …
Medicine Pulmonary alveolar proteinosis – current and future therapeutical strategies : Current …
Autoimmune pulmonary alveolar proteinosis
C McCarthy, BC Carey, BC Trapnell - American journal of …, 2022 - atsjournals.org
Autoimmune pulmonary alveolar proteinosis (PAP) is a rare disease characterized by
myeloid cell dysfunction, abnormal pulmonary surfactant accumulation, and innate immune …
myeloid cell dysfunction, abnormal pulmonary surfactant accumulation, and innate immune …
[HTML][HTML] Inhaled molgramostim therapy in autoimmune pulmonary alveolar proteinosis
BC Trapnell, Y Inoue, F Bonella… - … England Journal of …, 2020 - Mass Medical Soc
Background Autoimmune pulmonary alveolar proteinosis (aPAP) is a rare disease
characterized by progressive surfactant accumulation and hypoxemia. It is caused by …
characterized by progressive surfactant accumulation and hypoxemia. It is caused by …
[HTML][HTML] Inhaled recombinant GM-CSF reduces the need for whole lung lavage and improves gas exchange in autoimmune pulmonary alveolar proteinosis patients
I Campo, BC Carey, E Paracchini… - European …, 2024 - Eur Respiratory Soc
Rationale Whole lung lavage (WLL) is a widely accepted palliative treatment for
autoimmune pulmonary alveolar proteinosis (aPAP) but does not correct myeloid cell …
autoimmune pulmonary alveolar proteinosis (aPAP) but does not correct myeloid cell …
Genetic determinants of risk in autoimmune pulmonary alveolar proteinosis
S Sakaue, E Yamaguchi, Y Inoue, M Takahashi… - Nature …, 2021 - nature.com
Pulmonary alveolar proteinosis (PAP) is a devastating lung disease caused by abnormal
surfactant homeostasis, with a prevalence of 6–7 cases per million population worldwide …
surfactant homeostasis, with a prevalence of 6–7 cases per million population worldwide …
Pulmonary alveolar proteinosis: from classification to therapy
E Salvaterra, I Campo - Breathe, 2020 - Eur Respiratory Soc
Pulmonary alveolar proteinosis (PAP) is a rare respiratory syndrome characterised by the
accumulation of surfactant lipoproteins within the alveoli. According to various pathogenetic …
accumulation of surfactant lipoproteins within the alveoli. According to various pathogenetic …
European Respiratory Society guidelines for the diagnosis and management of pulmonary alveolar proteinosis
C McCarthy, F Bonella, M O'callaghan… - European …, 2024 - publications.ersnet.org
Background Pulmonary alveolar proteinosis (PAP) is a rare syndrome caused by several
distinct diseases leading to progressive dyspnoea, hypoxaemia, risk of respiratory failure …
distinct diseases leading to progressive dyspnoea, hypoxaemia, risk of respiratory failure …
Alveolar macrophages in pulmonary alveolar proteinosis: origin, function, and therapeutic strategies
X Huang, M Cao, Y Xiao - Frontiers in Immunology, 2023 - frontiersin.org
Pulmonary alveolar proteinosis (PAP) is a rare pulmonary disorder that is characterized by
the abnormal accumulation of surfactant within the alveoli. Alveolar macrophages (AMs) …
the abnormal accumulation of surfactant within the alveoli. Alveolar macrophages (AMs) …
Update on diagnosis and treatment of adult pulmonary alveolar proteinosis
Pulmonary alveolar proteinosis (PAP) is a rare pulmonary surfactant homeostasis disorder
resulting in buildup of lipo-proteinaceous material within the alveoli. PAP is classified as …
resulting in buildup of lipo-proteinaceous material within the alveoli. PAP is classified as …