Myelin deficiencies visualized in vivo: visually evoked potentials and T2weighted magnetic resonance images of shiverer mutant and wild‐type mice

M Martin, TD Hiltner, JC Wood… - Journal of …, 2006 - Wiley Online Library
… shiverer mice, μMRI can discern hypomyelination throughout … and micro-MRI (μMRI) in
tandem on a dysmyelinating mouse … tract, part of the visual pathway along which the VEPs travel. …

Role of neuronal activity and kinesin on tract tracing by manganese-enhanced MRI (MEMRI)

EL Bearer, TL Falzone, XW Zhang, O Biris, A Rasin… - Neuroimage, 2007 - Elsevier
… of mouse genetics and the simplicity of the visual system to test … weighted microMRI images
at 6-minute intervals in an 11.7 TVisual evoked potentials were measured before, and at 4 …

The mouse model of Down syndrome Ts65Dn presents visual deficits as assessed by pattern visual evoked potentials

JJ Scott-McKean, B Chang, RE Hurd… - … & visual science, 2010 - iovs.arvojournals.org
… of the binocular visual cortex of anesthetized mice in response to … , even though these animals
display severe hypomyelination of … Outcome measures for trials of remyelinating agents in …

Spontaneous ocular and neurologic deficits in transgenic mouse models of multiple sclerosis and noninvasive investigative modalities: a review

AA Gupta, D Ding, RK Lee, RB Levy… - … & visual science, 2012 - iovs.arvojournals.org
… An evoked response is an electrical potential recorded from … in an adult mouse visual
system characterized by modulation … evolution of MS lesions with T 1 - and T 2 -weighted MRI; …

Inborn errors of brain myelin formation

O Boespflug-Tanguy - Handbook of clinical neurology, 2013 - Elsevier
… a normal appearance on T1-weighted images, tends to be … of MRI and evoked potentials
suggesting a hypomyelinating … I and absence or small size of later components. Interestingly, …

[图书][B] Pediatric Neurology Part III: Chapter 162. Inborn errors of brain myelin formation

O Boespflug-tanguy - 2013 - books.google.com
… a normal appearance on T1weighted images, tends to be … of MRI and evoked potentials
suggesting a hypomyelinating … I and absence or small size of later components. Interestingly, …

Mutation of proteolipid protein 1 gene: From severe hypomyelinating leukodystrophy to inherited spastic paraplegia

G Khalaf, C Mattern, M Begou, O Boespflug-Tanguy… - Biomedicines, 2022 - mdpi.com
evoked potentials) and magnetic resonance imaging (MRI) to … : PLP1 duplications of different
sizes affecting 60% to 70% of … relative to gray matter on T1-weighted images and then from …

Pathophysiology and emerging therapeutic strategies in Pelizaeus–Merzbacher disease

H Osaka, K Inoue - Expert Opinion on Orphan Drugs, 2015 - Taylor & Francis
weighted images and from hyperintense to hypointense in T2… Diffuse and homogeneous
hypomyelination on the MRI is … or somatosensory evoked potentials), are helpful in the …

CLINICAL, MRI, AND SKIN BIOPSY FINDINGS IN SENSORY GANGLIONOPATHIES

A Sghirlanzoni, D Pareyson, M Grisoli… - … Nervous System, 2000 - Wiley Online Library
… To test the ability of CL to affect PL metabolism we have measured de … evoked potentials
showed the absence of C fibre potentials, … from transient perinatal hypomyelination (30% mRNA …

PATHOGENESIS OF CONGENITAL HYPOMYELINATION REVEALED BY P0 OVEREXPRESSING MICE

S Previtali, A Quattrini, D Imperiale… - … Nervous System, 2000 - Wiley Online Library
… affect PL metabolism we have measured de novo PL biosynthesis… evoked potentials showed
the absence of C fibre potentials, … A lumbosacral MRI showed a spinal stenosis and multiple …