Who are the long-QT syndrome patients who receive an implantable cardioverter-defibrillator and what happens to them? Data from the European Long-QT Syndrome …

PJ Schwartz, C Spazzolini, SG Priori, L Crotti… - Circulation, 2010 - Am Heart Assoc
Background—A rapidly growing number of long-QT syndrome (LQTS) patients are being
treated with an implantable cardioverter-defibrillator (ICD). ICDs may pose problems …

Implantable cardioverter defibrillator in highrisk long QT syndrome patients

W Zareba, AJ Moss, JP Daubert, WJ Hall… - Journal of …, 2003 - Wiley Online Library
Introduction: Implantable cardioverter defibrillators (ICDs) are increasingly being used in
highrisk long QT syndrome (LQTS) patients, but there are limited data regarding clinical …

Implantable cardioverter-defibrillator therapy in patients with congenital long-QT syndrome: a long-term follow-up

G Mönnig, J Köbe, A Löher, L Eckardt, H Wedekind… - Heart rhythm, 2005 - Elsevier
OBJECTIVES: The purpose of this study was to evaluate retrospectively a single-center
experience with the use of ICDs in patients with long QT syndrome (LQTS) concerning …

Implantable cardioverter defibrillator therapy for congenital long QT syndrome: a single-center experience

JM Horner, M Kinoshita, TL Webster, CM Haglund… - Heart Rhythm, 2010 - Elsevier
BACKGROUND: Long QT syndrome's (LQTS) marked heterogeneity necessitates both
evidence-based and individualized therapeutic approaches. OBJECTIVE: This study sought …

Long QT syndrome in children in the era of implantable defibrillators

SP Etheridge, S Sanatani, MI Cohen, CA Albaro… - Journal of the American …, 2007 - jacc.org
Objectives: We sought to assess the spectrum and outcome of young long QT syndrome
(LQTS) patients, addressing treatment including device indications, risks, and benefits …

Long QT syndrome and short QT syndrome

W Zareba, I Cygankiewicz - Progress in cardiovascular diseases, 2008 - Elsevier
The long QT syndrome (LQTS) is a genetic disorder characterized by prolongation of the QT
interval in the electrocardiogram (ECG) and a propensity to torsades de pointes ventricular …

Contemporary outcomes in patients with long QT syndrome

RK Rohatgi, A Sugrue, JM Bos, BC Cannon… - Journal of the American …, 2017 - jacc.org
Abstract Background: Long QT syndrome (LQTS) is a potentially lethal cardiac
channelopathy with a 1% to 5% annual risk of LQTS-triggered syncope, aborted cardiac …

Independent validation and clinical implications of the risk prediction model for long QT syndrome (1-2-3-LQTS-Risk)

A Mazzanti, A Trancuccio, D Kukavica, E Pagan… - EP …, 2022 - academic.oup.com
Aims Risk stratification of patients with long QT syndrome (LQTS) represents a difficult task.
In 2018, we proposed a granular estimate of the baseline 5-year risk of life-threatening …

Long QT syndrome: a comprehensive review of the literature and current evidence

SR Shah, K Park, R Alweis - Current problems in cardiology, 2019 - Elsevier
Long QT syndrome (LQT) represents a heterogeneous family of cardiac electrophysiologic
disorders characterized by QT prolongation and T-wave abnormalities on the …

Long QT syndrome

I Goldenberg, W Zareba, AJ Moss - Current problems in cardiology, 2008 - Elsevier
The hereditary Long QT syndrome (LQTS) is a genetic channelopathy with variable
penetrance that is associated with increased propensity for polymorphic ventricular …