Comparison of common monogenic defects in a large predominantly antibody deficiency cohort

R Yazdani, H Abolhassani, F Kiaee, S Habibi… - The Journal of Allergy …, 2019 - Elsevier
Background Predominantly antibody deficiencies (PADs) are the most common primary
immunodeficiencies, characterized by hypogammaglobulinemia and inability to generate …

Beyond monogenetic rare variants: tackling the low rate of genetic diagnoses in predominantly antibody deficiency

ESJ Edwards, JJ Bosco, S Ojaimi, RE O'Hehir… - Cellular & Molecular …, 2021 - nature.com
Predominantly antibody deficiency (PAD) is the most prevalent form of primary
immunodeficiency, and is characterized by broad clinical, immunological and genetic …

[HTML][HTML] Predominantly antibody deficiencies

G Azizi, R Yazdani - Immunology and Genetics Journal, 2018 - igj.tums.ac.ir
Primary antibody deficiencies (PADs) are frequent primary immunodeficiencies in humans,
characterized by hypogammaglobulinemia, defects in production of specific antibodies, and …

Immunological and clinical phenotyping in primary antibody deficiencies: a growing disease spectrum

JJ Shin, D Liauw, S Siddiqui, J Lee, EJ Chung… - Journal of clinical …, 2020 - Springer
Purpose Although common variable immunodeficiency (CVID) is considered the most
prevalent symptomatic primary antibody deficiency (PAD), there is a population with …

[HTML][HTML] Protocol for the unclassified primary antibody deficiency (unPAD) study: Characterization and classification of patients using the ESID online Registry

LMA Janssen, ICGM Reijnen, C Milito, D Edgar… - Plos one, 2022 - journals.plos.org
Background Primary antibody deficiencies (PADs) without an identified monogenetic origin
form the largest and most heterogeneous group of primary immunodeficiencies. These …

[HTML][HTML] Defects in memory B-cell and plasma cell subsets expressing different immunoglobulin-subclasses in patients with CVID and immunoglobulin subclass …

E Blanco, M Pérez-Andrés, S Arriba-Méndez… - Journal of Allergy and …, 2019 - Elsevier
Background Predominantly antibody deficiencies (PADs) are the most prevalent primary
immunodeficiencies, but their B-cell defects and underlying genetic alterations remain …

There is no gene for CVID—novel monogenetic causes for primary antibody deficiency

NJ Ramirez, S Posadas-Cantera… - Current Opinion in …, 2021 - Elsevier
'There is no gene for fate'(citation from the movie 'GATTACA')—and there is no gene for
CVID. Common Variable ImmunoDeficiency (CVID) is the most prevalent primary …

The clinical and immunological features of patients with primary antibody deficiencies

G Azizi, Y Bagheri, M Tavakol… - … Metabolic & Immune …, 2018 - ingentaconnect.com
Background: Primary antibody deficiency (PAD) comprises a range of diseases from early to
late terminal B cells defects and is associated with the various clinical complications …

Advances and highlights in primary immunodeficiencies in 2017

J Chinen, MJ Cowan - Journal of Allergy and Clinical Immunology, 2018 - Elsevier
This manuscript reviews selected topics in primary immunodeficiency diseases (PIDDs)
published in 2017. These include (1) the role of follicular T cells in the differentiation of B …

New facets of antibody deficiencies

K Liadaki, J Sun, L Hammarström… - Current opinion in …, 2013 - Elsevier
Highlights•Nine novel genetic defects are described for antibody deficiencies.•Dysregulated
autophagy maybe a novel mechanism underlying antibody deficiencies.•Next generation …