Background—Ebstein anomaly is a rare congenital heart malformation characterized by
adherence of the septal and posterior leaflets of the tricuspid valve to the underlying …

Left ventricular noncompaction (LVNC) is a relatively common genetic cardiomyopathy,
characterized by prominent trabeculations with deep intertrabecular recesses in mainly the …

Ebstein's anomaly is uncommon. Genetic bases of this congenital heart defect may be
related to the mutations in myosin heavy chain 7 and NKX2. 5, among others. Asymptomatic …

OBJECTIVE To identify the incidence of left heart abnormalities in patients with Ebstein
anomaly, recognizing that left-sided lesions in this patient group have been overlooked …

BACKGROUND: Noncompaction of the ventricular myocardium is a rare congenital
cardiomyopathy characterized by numerous excessively prominent trabeculations and deep …

Background—Mutations in the genes encoding sarcomere proteins have been associated
with both hypertrophic and dilated cardiomyopathy. Recently, mutations in myosin heavy …

Exercise intolerance in Ebstein's anomaly is usually attributed to desaturation secondary to
right-to-left shunting as a result of a small or distorted left ventricle (LV), significant tricuspid …

Background—Left ventricular noncompaction constitutes a primary cardiomyopathy
characterized by a severely thickened, 2-layered myocardium, numerous prominent …

Background—The molecular underpinnings of hypoplastic left heart are poorly understood.
Staged surgical palliation has dramatically improved survival, yet eventual failure of the …

Noncompaction of the ventricular myocardium (NVM) is the morphological hallmark of a rare
familial or sporadic unclassified heart disease of heterogeneous origin. NVM results …