… : Left ventricular hypertrabeculation (LVHT) has not been described in myotonic dystrophy
Type I (… a heterozygous 300 CTGrepeat expansion in the myotonic-dystrophy proteinkinase …

… Congenital left ventricular hypertrabeculation/noncompaction (LVHT) is a common feature of
neuromuscular … In myotonic dystrophy type 1 (MD1) acquired LVHT has not been described. …

… myotonic dystrophy type 2 (DM2) with dilated cardiomyopathy and severe arrhythmias having
been reported. Left ventricular … MRI confirmed LV hypertrabeculation, LV hypokinesis and …

… Background: Familial left ventricular hypertrabeculation (LVHT) has not been described
in myotonic dystrophy type 1 (MD1). Case Report: Two MD1 patients are described, father …

… (n=3), myotonic dystrophy (n=2) and Becker muscular dystrophy (n=1). Those patients in …
were brothers and two patients with myotonic dystrophy were father and daughter. In group …

… LVHT has been described in 2 patients with myotonic dystrophy type 1 so far. The first
patient was a 42-year-old man with typical features of myotonic dystrophy type 1 since age 34 …

… failure is uncommon in patients with MD1 compared to other muscular dystrophies[7, 8],
left ventricular systolic dysfunction is associated with an increased risk of overall mortality and …

… In rare cases, however, >3 trabeculations are found by autopsy or echocardiography in
the left ventricle. Left ventricular hypertrabeculation (LVHT) is easily overlooked, even by …

… present with cardiac disease [1], left ventricular hypertrabeculation / noncompaction (LVHT)
has … Left ventricular hypertrabeculation in myotonic dystrophy type 1. Herz 2001; 26: 287-90. …

… mitochondrial disorders, Barth syndrome, zaspopathy, and myotonic dystrophy type 1. LVHT
does not seem to be a special type of cardiac involvement of NMDs. NMDs affect prognosis …